This case report discusses pharmacological options and management strategies for electrical storm in a pediatric patient with CPVT and an ICD.
Hypothesis-generating for pharmacological strategies in pediatric CPVT electrical storm; prospective data needed before clinical adoption.
We present a case of a young boy who had an implantable cadrioverter defibrillator implanted for refractory syncope and cathecolaminergic polymorphic ventricular tachycardia (CPVT). The patient underwent an electrical storm with multiple shocks and serious compromise of quality of life and risk. The pharmacological options are discussed as well as the strategies of managing ventricular arrhythmias in CPVT.
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Fagundes et al. (2009) studied this question.
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