Bilateral adrenalectomy is an effective treatment for primary pigmented nodular adrenocortical disease, a rare cause of ACTH-independent Cushing's syndrome.
Bilateral adrenalectomy may be effective for pediatric PPNAD; single case leaves open need for confirmatory studies.
Primary pigmented nodular adrenocortical disease (PPNAD) is a rare cause of ACTH-independent Cushing's syndrome and has characteristic gross and microscopic pathologic findings. We report a case of PPNAD in a 15-year-old boy, which was not associated with Carney's complex. Bilateral adrenalectomy is the treatment of choice.
No takes yet. Share an insight, caveat, or question.
Manipadam et al. (2011) studied this question.