This case report details the presentation and management of two cases of dermatofibrosarcoma protuberans, a rare cutaneous neoplasm.
Site-specific DFSP cases highlight diagnostic vigilance; extends sparse literature but leaves open need for larger studies before practice change.
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm with a high frequency of recurrence after inadequate primary treatment.It is most commonly seen in individuals in their third to fifth decades but has been reported in all age groups.Literatures regarding Dermatofibrosarcoma protuberans accounts for less than 0.1% of all malignant neoplasms and approximately 1% of all soft tissue sarcomas.The incidence has been estimated to be 0.8 to 5 cases per 1 million people per year.A wide-margin surgical excision with microscopically disease-free margins is the standard treatment.We report two cases of dermatofibrosarcoma protuberans at different sites of the body and present a detailed discussion of the diagnosis, treatment and outcomes with reference to available literatures.
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Zakaria et al. (2012) studied this question.
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