Isolated left ventricular noncompaction should be considered in the differential diagnosis of pediatric patients presenting with left ventricular wall akinesis.
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May support considering isolated LV noncompaction in pediatric LV akinesis differentials; hypothesis-generating pending larger confirmatory studies.
A 12-year-old boy presented with isolated noncompaction of the ventricular myocardium (INVM), a rare cardiomyopathy of childhood. Echocardiography revealed spongy myocardium with deep intratrabecular recesses at the left ventricular apex. Gated blood-pool scintigraphy revealed an akinetic lateral wall and apex with a normal ejection fraction.
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Fagen et al. (2005) studied this question.
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