Population
2 patients with lymphangiosarcoma arising in a chronic lymphedematous extremity following mastectomy for…
Design
Case_series
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Supports vascular endothelial origin in Stewart-Treves tumors; leaves open diagnostic reclassification and management implications pending larger studies.
Stewart-Treves syndrome tumors originate from vascular endotheliocytes despite appearing to derive from lymphatic vessels, and require radical surgical amputation due to rapid multicentric spread.
Tomita et al. (1988) studied this question.
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