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April 1, 1999Muscle & Nerve

Quantitative electrophysiologic studies in sporadic inclusion body myositis

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Why the study?

Do quantitative electrophysiologic studies in sporadic inclusion body myositis indicate a myopathic or neurogenic process?

Population

17 subjects with biopsy-proven sporadic inclusion body myositis (S-IBM)

Design

Cross-sectional

Authors

PBPaul E. BarkhausMedical College of WisconsinMPM. Isabel PeriquetSNSanjeev D. NandedkarMedical College of Wisconsin

Discussion

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Implication

Supports myopathic EMG classification in S-IBM; leaves open prospective validation and diagnostic algorithm impact.

Structured PICO

Do quantitative electrophysiologic studies in sporadic inclusion body myositis indicate a myopathic or neurogenic process?

P
Population
17 subjects with biopsy-proven sporadic inclusion body myositis (S-IBM)
I
Intervention
Quantitative electrophysiologic studies in the biceps brachii (including quantitative motor unit action potential analysis, quantitative interference pattern, Macro-EMG, and fiber density)
O
Outcome
Electrophysiologic characteristics (myopathic vs neurogenic pattern)surrogate

Quantitative electrophysiologic studies confirm that sporadic inclusion body myositis is primarily a myopathic rather than neurogenic process.

Cite This Study

Barkhaus et al. (1999) studied this question.

synapsesocial.com/papers/6a92a90d29f7ca37161f6e59https://doi.org/10.1002/(sici)1097-4598(199904)22:4<480::aid-mus9>3.0.co;2-a
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Quantitative EMG in inflammatory myopathy1990 · 59 citations
  2. 2Inclusion body myositis (IBM)1983 · 95 citations
  3. 3DAX-1 Gene Mutations and Deletions in Japanese Patients with Adrenal Hypoplasia Congenita and Hypogonadotropic Hypogonadism1997 · 25 citations
  4. 4Invited review: Electrodiagnostic assessment and monitoring of motor unit changes in disease1991 · 46 citations
  5. 5The terminal innervation pattern in polymyositis: A histochemical and SFEMG study1978 · 67 citations