Syndrome de Sturge-Weber bilatéral : aspects cliniques et scanographiques à propos de deux cas

The Sturge-Weber syndrome associated a facial port-wine stain skin on the territory of the trigeminal nerve (V1), a venous lepto-meningeal angioma and ipsilateral choroidal angioma. We report two cases of Sturge Weber syndrome in two children aged 14 months and 45 months with bilateral involvement of the trigeminal territory. We emphasized the difficulty of clinical diagnosis due to poor detection of facial port-wine stain skin on black skin and the central role of diagnostic imaging. Both cases were diagnosed during a CT-scan for epilepsy with hemiparesis. Skin lesions were identified after the imaging diagnosis in the first case.