Key result
A 49-year-old woman presented with metastatic primary right atrial angiosarcoma, highlighting the difficulties in diagnosis and management due to non-specific presentation and lack of guidelines.
Why the study?
Diagnosis of primary cardiac angiosarcoma is often delayed due to non-specific presentation, and evidence-based treatment guidelines have yet to be established due to the rarity of the tumour.
Case Report (n=1)
Primary cardiac angiosarcoma is a rare tumor with a poor prognosis due to delayed diagnosis and a lack of established evidence-based treatment guidelines.
Case cautions against delayed diagnosis in non-specific cardiac presentations; leaves open prospective data for evidence-based angiosarcoma management.
We report a 49-year-old Southeast Asian woman diagnosed with metastatic primary right atrial angiosarcoma (PCA) and the difficulties encountered in this diagnosis and its subsequent management. Diagnosis of PCA is often delayed due to non-specific clinical presentation of patients. These tumours often present once metastatic spread has occurred, restricting treatment options and leading to very poor prognosis. Patients undergo a multidisciplinary team (MDT) approach involving chemotherapy, radiotherapy and, if eligible, surgery, but evidence-based treatment guidelines have yet to be established due to the rarity of the tumour.
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Intrator et al. (2021) conducted a case report in Metastatic primary right atrial angiosarcoma (n=1). Multidisciplinary team approach (chemotherapy, radiotherapy, surgery) was evaluated. A 49-year-old woman presented with metastatic primary right atrial angiosarcoma, highlighting the difficulties in diagnosis and management due to non-specific presentation and lack of guidelines.
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