Key result
Surgical resection of a massive cardiac undifferentiated pleomorphic sarcoma was complicated by incomplete resection and rapid metastasis, leading to death 117 days after surgery.
Why the study?
Malignant tumors originating from the heart are extremely rare.
Case Report (n=1)
No
Primary cardiac undifferentiated pleomorphic sarcoma is a rare, aggressive malignancy that can present with severe RVOT obstruction and has a poor prognosis despite extensive surgical resection.
Portends poor survival after incomplete resection of cardiac sarcomas; leaves open optimal management strategies.
Malignant tumors originating from the heart are extremely rare. Here, we report a case of severe right ventricular outflow tract (RVOT) stenosis in a 67 year-old woman caused by a massive intimal sarcoma that required venous-arterial extracorporeal membrane oxygenation to support systemic circulation. Surgical resection and RVOT reconstruction with tricuspid and pulmonary valve replacement were performed. The pathological diagnosis was cardiac undifferentiated pleomorphic sarcoma. Although the patient was discharged 65 days after surgery in good condition, she subsequently died from multiple metastases detected in the early phase after surgery.
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Yoshida et al. (2023) conducted a case report in Cardiac undifferentiated pleomorphic sarcoma with right ventricular outflow tract obstruction (n=1). Surgical resection and right ventricular outflow tract reconstruction was evaluated on Clinical outcome. Surgical resection of a massive cardiac undifferentiated pleomorphic sarcoma was complicated by incomplete resection and rapid metastasis, leading to death 117 days after surgery.
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