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November 18, 2019CJC OpenOpen Access

Prognostic Implications of Left Ventricular Cardiomyopathy in Adults With Tetralogy of Fallot

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Why the study?

Despite significant cardiovascular mortality after tetralogy of Fallot repair, data on the risk and prognostic implications of left ventricular cardiomyopathy were limited.

Does left ventricular systolic dysfunction increase the risk of cardiovascular events in adult patients after tetralogy of Fallot repair?

Population

574 adult patients after TOF repair with echocardiographic LVEF assessment

Comparison

Left ventricular systolic dysfunction vs preserved LVEF

Design

Cohort study

Follow-up

10.5 ± 6.2 years

Key result

A 5%-point decrease in left ventricular ejection fraction was an independent predictor of mortality (HR 1.16; 95% CI 1.16-1.24; P=0.003) in adults after tetralogy of Fallot repair.

Authors

AEAlexander C. EgbePPPatricia A. PellikkaAAArslan Afzal

Discussion

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Member takes

Overview

May warrant closer LVEF monitoring in adult TOF survivors; leaves open whether LV-targeted therapy alters mortality.

Study Design

Type

Cohort (n=574)

Structured PICO

Does left ventricular systolic dysfunction increase the risk of cardiovascular events in adult patients after tetralogy of Fallot repair?

P
Population
574 adult patients after tetralogy of Fallot repair with echocardiographic assessment of LVEF, followed for a mean of 10.5 years.
E
Exposure
Left ventricular systolic dysfunction (LVD), defined as LVEF < 50% at baseline or new decrease to < 50% during follow-up
C
Comparator
Preserved LVEF (LVEF ≥ 50%)
O
Outcome
Cardiovascular events, defined as sustained ventricular tachycardia, aborted sudden death, heart transplantation, or deathcomposite

Main Result

Hazard Ratio: 1.16 (95% CI 1.16–1.24)

p-value: p=0.003

Left ventricular systolic dysfunction is present in a significant minority of adults after TOF repair and is independently associated with increased cardiovascular mortality and events.

Cite This Study

Egbe et al. (2019) conducted a cohort in Tetralogy of Fallot (TOF) repair (n=574). Left ventricular systolic dysfunction (LVD) / LVEF decrease vs. Preserved LVEF was evaluated on Mortality (HR 1.16, 95% CI 1.16-1.24, p=0.003). A 5%-point decrease in left ventricular ejection fraction was an independent predictor of mortality (HR 1.16; 95% CI 1.16-1.24; P=0.003) in adults after tetralogy of Fallot repair.

synapsesocial.com/papers/6a9b454cb893971f7a7e35e5https://doi.org/10.1016/j.cjco.2019.11.004
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