Key result
The Mustard operation performed at age 12 for complete transposition of the great arteries was followed by an uneventful 8-year course before fatal late right ventricular failure occurred.
Case Report (n=1)
Documents a rare case of late right (systemic) ventricular failure and death 8 years after a successful Mustard operation for transposition of the great arteries.
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Late systemic RV failure remains a concern after Mustard repair; leaves open optimal surveillance strategies for transposition survivors.
Nixon et al. (1978) conducted a case report in Complete transposition of the great arteries (n=1). Mustard operation was evaluated on Late right ventricular failure and death. The Mustard operation performed at age 12 for complete transposition of the great arteries was followed by an uneventful 8-year course before fatal late right ventricular failure occurred.
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