Double Outlet Right Ventricle

Double outlet right ventricle (DORV) is characterized by an abnormal connection between both great arteries and the right ventricle, leading to poor systemic oxygenation. The diagnostic criteria for this condition vary, as do the various morphologies that exist. Echocardiography is the primary imaging tool, requiring views from multiple planes to elucidate the specific morphology of DORV in each patient, along with any associated cardiac anomalies. Incorporating other imaging modalities such as CT to maximize diagnostic accuracy is essential in determining the proper surgical approach, as the survival rate for children who undergo surgical repair remains high.