Key result
A 24-year-old postpartum woman with Marfan's syndrome developed a rapidly expanding abdominal aortic aneurysm 3 months after delivery and a Stanford type B thoracic aortic dissection one year postpartum despite beta-blocker therapy.
Case Report (n=1)
This case highlights the rare but severe risk of developing both a true abdominal aortic aneurysm and thoracic aortic dissection in the postpartum period in women with Marfan's syndrome, emphasizing the need for careful follow-up and imaging of the entire aorta.
May support intensified postpartum aortic surveillance in Marfan syndrome; leaves open optimal protocols.
A 24-year-old pregnant woman with Marfan's syndrome delivered by cesarean section during the 38th week of gestation. Although aortic root dilatation did not increase during pregnancy, three months after delivery, the patient noticed a pulsatile abdominal mass. Aortic aneurysm was diagnosed and surgical replacement of the infrarenal abdominal aorta to the common iliac arteries and reconstruction of the inferior mesenteric artery were performed. Moreover, the patient subsequently developed a Stanford type B thoracic aortic dissection, even after more than four months of beta-blockade.
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Tomihara et al. (2006) conducted a case report in Marfan's syndrome (n=1). Pregnancy and postpartum state was evaluated on Development of aortic aneurysm and dissection. A 24-year-old postpartum woman with Marfan's syndrome developed a rapidly expanding abdominal aortic aneurysm 3 months after delivery and a Stanford type B thoracic aortic dissection one year postpartum despite beta-blocker therapy.
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