Key result
Undiagnosed Marfan syndrome presents as fatal aortic root dissection 13 days after uneventful childbirth.
Case Report (n=1)
Highlights the critical importance of antenatal diagnosis and monitoring of Marfan syndrome to prevent fatal postpartum aortic dissection.
Supports heightened postpartum aortic vigilance in suspected Marfan syndrome; leaves open optimal screening and surveillance protocols.
Aortic dissection in pregnancy is a lethal cardiovascular complication in women with Marfan syndrome. The course of the treatment would be decided upon by the size of aortic root dilation. We report a case where the unawareness of the diagnosis of Marfan syndrome antenatally led to disastrous post partum consequences even after an uneventful childbirth. DOI: http://dx.doi.org/10.4038/sljog.v34i2.4829 Sri Lanka Journal of Obstetrics and Gynaecology 2012; 34: 55-57
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Nishad et al. (2012) conducted a case report in Undiagnosed Marfan syndrome with dissecting aortic root aneurysm (n=1). Pregnancy in undiagnosed Marfan syndrome was evaluated on Maternal mortality due to aortic dissection. An undiagnosed 37-year-old woman with Marfan syndrome suffered a fatal dissecting aortic root aneurysm on the thirteenth postpartum day despite an uneventful childbirth.
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