Key result
Fatal pediatric cor triatriatum dexter with PH highlights the need for early surgical referral.
Why the study?
Cor triatriatum dexter is a rare congenital heart defect with limited clinical reports describing its presentation and outcomes, especially when complicated by pulmonary hypertension.
Case Report (n=1)
This case highlights the critical need for early diagnosis and prompt referral of patients with Cor triatriatum dexter to prevent mortality from a defect amenable to simple corrective surgery.
Fatal pediatric case of cor triatriatum dexter with pulmonary hypertension supports diagnostic vigilance; leaves open optimal timing of intervention in rare congenital anomalies.
Cor triatriatum (CT) otherwise known as a tri atrial heart is a rare congenital heart defect. This report describes a rare case of CT dexter in a 2-year-old girl who presented to our facility with cough and difficulty in breathing of a year duration and body swelling of 3 months duration. She was also found to be in heart failure. Transthoracic echocardiography revealed a membrane separating the right atrium into two chambers, with features of pulmonary hypertension. Although the patient was scheduled for follow-up, she however, died 2 days later. Early diagnosis and prompt referral of patients with this rare defect are mandatory to prevent mortality from this defect that is amenable to simple corrective surgery.
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Asani et al. (2016) conducted a case report in Cor triatriatum dexter with pulmonary hypertension (n=1). Cor triatriatum dexter was evaluated on Clinical course / Mortality. A 2-year-old girl diagnosed with Cor triatriatum dexter and pulmonary hypertension died 2 days after presentation, highlighting the need for early diagnosis and prompt referral for corrective surgery.
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