Key result
Urgent on-pump CABG successfully treats NSTEMI in a patient with vascular Ehlers-Danlos syndrome.
Why the study?
There are no prior reports of successful on-pump coronary artery bypass surgery in patients with vascular Ehlers-Danlos syndrome presenting with myocardial infarction.
Case Report (n=1)
No
This represents the first reported case of successful on-pump CABG surgery in a patient with vascular Ehlers-Danlos syndrome.
May support considering on-pump CABG in select vEDS patients with NSTEMI; leaves open safety, generalizability, and need for prospective data.
A 58-year-old woman with vascular Ehlers-Danlos syndrome (EDS; type IV) presented to a Canadian tertiary care emergency department with a non-ST elevation myocardial infarction. The patient failed medical therapy and after careful consideration of the options, elected to undergo urgent coronary artery bypass (CABG) surgery. To the best of our knowledge, this is the first reported case of a successful on-pump CABG surgery in a patient with vascular EDS.
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Kelly et al. (2014) conducted a case report in Vascular Ehlers-Danlos syndrome and non-ST elevation myocardial infarction (n=1). On-pump coronary artery bypass (CABG) surgery was evaluated on Successful surgery. Urgent on-pump coronary artery bypass (CABG) surgery was successfully performed in a 58-year-old woman with vascular Ehlers-Danlos syndrome and non-ST elevation myocardial infarction.
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