Key result
Minimally invasive mitral valve repair proves feasible in Marfan syndrome with type B dissection.
Why the study?
It is unclear whether full sternotomy and prophylactic aortic surgery are necessary for Marfan syndrome patients with mitral regurgitation without type A dissection or aortic root dilation.
Case Report (n=1)
Minimally invasive mitral valve repair can be a successful and less invasive alternative to full sternotomy in selected patients with Marfan syndrome and type B dissection.
Minimally invasive mitral repair may be feasible in select Marfan cases with type B dissection; leaves open whether sternotomy or prophylactic aortic surgery can be avoided.
We report the case of a patient with mitral regurgitation complicated by type B dissection and Marfan syndrome (MFS) who was managed successfully with minimally invasive mitral valve repair. Without type A aortic dissection or aortic root dilation, MFS patients may develop mitral valve regurgitation, as in this case, and need valve surgery to improve their symptoms and long-term survival. However, it is not clear that a full sternotomy and prophylactic aortic surgery are necessary. Although retrograde perfusion to the dissected aorta is controversial, our approach minimizes the risk of future anticipated aortic surgery in MFS patients.
No takes yet. Share an insight, caveat, or question.
Lim et al. (2018) conducted a case report in Mitral regurgitation complicated by type B dissection and Marfan syndrome (n=1). Minimally invasive mitral valve repair was evaluated. Minimally invasive mitral valve repair was successfully performed in a woman with Marfan syndrome, mitral regurgitation, and type B dissection.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: