Key result
Endogenous PrPC expression profoundly affects the antibody repertoire, as B cells reactive for epitopes exposed on native PrPC are strongly tolerized in wild-type mice compared to Prnp o/o mice.
Population
Wild-type and PrP knockout (Prnp o/o) C57BL/6 mice
Comparison
Immunization with mouse PrP-plasmid DNA or with… vs Comparison between wild-type and Prnp o/o mice…
Design
Preclinical
Authors
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Suggests caution for PrPC-targeted immunotherapies; leaves open translation from mouse tolerance data to human prion disease.
Endogenous PrPC expression profoundly affects the antibody repertoire by strongly tolerizing B cells reactive to epitopes exposed on native PrPC, impacting potential immunotherapy strategies for prion diseases.
Grégoire et al. (2005) studied Prion disease / immune response to PrP. Immunization with mouse PrP-plasmid DNA or 30-mer overlapping peptides vs. Wild-type vs Prnp o/o mice was evaluated on Antibody and T cell repertoires directed to PrP. Endogenous PrPC expression profoundly affects the antibody repertoire, as B cells reactive for epitopes exposed on native PrPC are strongly tolerized in wild-type mice compared to Prnp o/o mice.
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