Key result
Surgical resection via median sternotomy was performed for a massive mediastinal liposarcoma in a 64-year-old man, with tumor recurrence observed 4 months postoperatively.
Case Report (n=1)
No
Surgical resection of a massive mediastinal liposarcoma is feasible, but the pleomorphic subtype carries a poor prognosis with early local recurrence.
Early recurrence after resection signals poor prognosis in pleomorphic mediastinal liposarcoma; leaves open optimal multimodal strategies for future cases.
症例は67歳,男性.高血圧にて近医経過観察中に心窩部不快感出現.超音波検査,胸部レントゲンにて右中~下肺野に超手拳大の腫瘤を指摘され当院紹介となった.CTにて右胸腔~縦隔右側にかけて160×110mmの腫瘤を認めた.腫瘤は上大静脈,右房を圧排し,心膜,横隔膜への浸潤も疑われた.CTガイド下生検施行しspindle cell sarcomaの診断で手術が施行された.左側臥位にて審査胸腔鏡施行後,摘除可能と判断し,仰臥位,胸骨正中切開にて摘出術施行した.術後経過は良好で,第15病日に退院となった.術後病理検査にて脂肪肉腫と診断された.今回比較的まれな縦隔発生の脂肪肉腫の1手術症例を経験したので報告する.
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Gorai et al. (2010) conducted a case report in Mediastinal liposarcoma (n=1). Surgical resection was evaluated. Surgical resection via median sternotomy was performed for a massive mediastinal liposarcoma in a 64-year-old man, with tumor recurrence observed 4 months postoperatively.
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