Key result
Ajmaline challenge unmasked a Brugada pattern in 25% (3 of 12) of adult patients with myotonic dystrophy type 1.
Why the study?
Does ajmaline challenge unmask Brugada pattern in patients with Myotonic Dystrophy Type 1?
Population
12 adult patients with Myotonic Dystrophy Type 1 with PR interval >200 ms or QRS duration >100 ms, no…
Design
Case_series
Follow-up
15 ± 4 months
Authors
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Suggests possible Brugada overlap; leaves open ajmaline challenge for sudden cardiac death risk stratification in myotonic dystrophy type 1 pending larger studies.
Observational (n=12)
No
Does ajmaline challenge unmask Brugada pattern in patients with Myotonic Dystrophy Type 1?
Ajmaline challenge unmasked a Brugada pattern in a subset of patients with Myotonic Dystrophy Type 1, suggesting a potential role in sudden cardiac death risk stratification.
Pambrun et al. (2014) conducted an observational in Myotonic dystrophy type 1 (n=12). Ajmaline challenge was evaluated on Unmasking of Brugada pattern. Ajmaline challenge unmasked a Brugada pattern in 25% (3 of 12) of adult patients with myotonic dystrophy type 1.
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