Key result
Surgical resection of a large intracardiac undifferentiated pleomorphic sarcoma with MDM2 amplification was followed by rapid tumor recurrence and death 9 months after diagnosis.
Case Report (n=1)
Primary undifferentiated pleomorphic cardiac sarcoma with MDM2 amplification is a rare, aggressive tumor with a grim prognosis despite surgical resection.
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Emphasizes aggressive behavior of resected intracardiac pleomorphic sarcoma; leaves open optimal management for this rare MDM2-amplified entity.
Watson et al. (2018) conducted a case report in Primary undifferentiated pleomorphic cardiac sarcoma with MDM2 amplification (n=1). Surgical resection was evaluated on Clinical course and survival. Surgical resection of a large intracardiac undifferentiated pleomorphic sarcoma with MDM2 amplification was followed by rapid tumor recurrence and death 9 months after diagnosis.